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.com
Volume 7, Issue 4 (Suppl)
Otolaryngology
ISSN: 2161-119X Otolaryngology, an open access journal
Aesthetic Medicine & ENT Conference 2017
July 06-08, 2017
July 06-08, 2017 Kuala Lumpur, Malaysia
International Conference on
Aesthetic Medicine and ENT
A Langerhans cell histiocytosis in its rare Letterer-Siwe form in a child mimicking an otoantritis: A case
report and literature review
M Bouali, H Mezhoud, H Soltani and I Fergoug
Oran University Hospital, Algeria
L
angerhans cell histiocytosis (LCH) is a group of three rare diseases (annual incidence less than 4/1000.000 H) with increasing
aggressiveness respectively: Eosinophilic granuloma (unifocal solitary osteolytic lesion), Hand-Schuller-Christian disease
(multifocal lesion) and Letterer-Siwe disease (the most aggressive, disseminated disease with systemic manifestations). The bone
is the most commonly involved with a predilection for the skull. Some cases of temporal bone localisations have been described
in the literature. We report a case of an 18 month child presenting a LCH of the temporal bone misdiagnosed at the beginning
as an otoantritis. In fact, the child presented a retro-auricular swelling with inflammatory characters, fever and otorrhea. The
exploration before surgery revealed besides the extensive temporal lesion, hematologic perturbations, a splenomegaly and a
hepatomegaly. The histopathology confirmed the diagnosis of a LCH. We describe the diagnosis challenges, the surgical
difficulties and the therapeutic response of the child and give a review of what was published on LCH and Letterer-Siwe disease.
Biography
M Bouali is currently working as faculty of medicine in department of Otorhinolaryngology at Oran University, Algeria.
emailbouali@gmail.comM Bouali et al., Otolaryngology 2017, 7:4 (Suppl)
DOI: 10.4172/2161-119X-C1-020