Unilateral Absence of Left Pulmonary Artery with Absent Pulmonary Valve Syndrome: Surgical Perspective on Primary Repair
Received Date: Jun 08, 2021 / Accepted Date: Jun 22, 2021 / Published Date: Jun 29, 2021
Abstract
Tetralogy of Fallot (TOF) with absent pulmonary valve and unilateral absence of pulmonary artery is an extremely rare congenital cardiac anomaly. Historically, the outcome of surgery in this subset has been very dismal. We believe valveless reconstruction for Right Ventricular Outflow Tract (RVOT) as a part of primary repair should never be opted for in this variant. Only a fully competent and durable valve in RVOT can provide meaningful early and time related survival in this variant. We report our experience with a bi-leaflet pulmonary valve constructed from 0.1 mm PTFE membrane in this substrate.
Keywords: Tetralogy of Fallot (TOF); Absent left pulmonary artery; Absent Pulmonary Valve (APV); Congenital heart surgery
Citation: Mahajan S, Khanna S, Patel R, Halder V, Bansal V (2021) Unilateral Absence of Left Pulmonary Artery with Absent Pulmonary Valve Syndrome: Surgical Perspective on Primary Repair. J Card Pulm Rehabil 5: 144. Doi: 10.4172/jcpr.1000144
Copyright: © 2021 Mahajan S, et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.
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