Abstract

A 65-year-old gentleman with Hereditary Haemorrhagic Telangiectasia (HHT) was referred for urgent mitral valve surgery because of septicaemia and congestive cardiac failure. After treating with antibiotics for three weeks, he underwent mitral valve repair by resection of prolapsed leaflet and neochordae implantation. Because of the presence of pharyngeal telangiectasia, intraoperative imaging of the repaired valve was achieved using epicardial echocardiography. This is the first reported experience, to the best of our knowledge, of a mitral valve repair in a patient with Hereditary Haemorrhagic Telangiectasia (HHT).