Malignant Orofacial Swelling in 4 Year Old Girl

¹Department of Pediatrics, Chacha Nehru Bal Chikitsalaya, New Delhi, India

²Department of Pediatrics, AIIMS, New Delhi, India

*Corresponding Author:

Rachna Seth
Department of Pediatrics
AIIMS, New Delhi-110029
India
Tel: 8447594629
E-mail: dramit_amy@yahoo.co.in

Received date: July 29, 2016; Accepted date: July 30, 2016; Published date: August 2, 2016

Citation: Rachna Seth (2016) Malignant Orofacial Swelling in 4 Year Old Girl,J Clin Diagn Res 4:I102. doi: 10.4172/2376-0311.1000I102

Copyright: © 2016, Amitabh Singh, et al. This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.

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Rhabdomyosarcoma of Oral Cavity

A 3 year-old girl presented with complaints of acute onset, rapidly progressive, painless swelling of orofacial region for 2 months. Local examination revealed a firm, protruding soft tissue mass arising from upper jaw involving upper lip, gums and nostril (Figure 1). Contrast enhanced CT scan of face revealed a well-defined midline anterior maxillary soft tissue mass with bony erosion and biopsy from the lesion confirmed the diagnosis of Rhabdomyosarcoma-embryonal type. Metastatic work up was negative. The mass showed complete shrinkage after 9 weeks of chemotherapy. Presently child is undergoing chemotherapy and is planned for radiotherapy. Rhabdomyosarcoma, the most common soft tissue sarcoma, accounts for 3-4% of all childhood cancers. RMS of oral cavity is rare and constitutes 10-12% of all head and neck Rhabdomyosarcoma. Standard therapy for Rhabdomyosarcoma includes chemotherapy combined with surgical resection+radiotherapy.

Figure 1: Soft tissue mass involving upper jaw, lip and nostrils.